Swelling was clinically visible during valsalva only. [11]. This condition is being increasingly recognized in recent years due to better imaging facilities [].There is a controversy about its etiology because there have been only sporadic reports of venous ectasia in the neck. Our report describes right internal jugular vein ectasia in a 15-year-old girl who presented to us with intractable paroxysmal cough. Internal jugular vein ectasia is a venous anomaly commonly presenting as a unilateral neck swelling in children and adults. Internal jugular vein (IJV) ectasia is a rare benign disease. Accessibility The condition can be diagnosed by imaging studies in particular during a Valsalva maneuver. 2, American Journal of Otolaryngology, Vol. Anatomically, Jugular vein ectasia have been described in the following sequence in frequency: internal jugular, external jugular, anterior jugular and superficial communi-cans [6]. 68, No. 2006 Sep;192(3):286-90. doi: 10.1016/j.amjsurg.2006.02.025. 1997 Jan 3;38(3):273-80. doi: 10.1016/s0165-5876(96)01455-3. Neck swellings that appear on straining, crying, and Valsalva maneuver are usually suggestive of laryngocele. It is rare to have bilateral neck swelling due to internal jugular vein ectasia. 3, International Journal of Pediatric Otorhinolaryngology, Vol. Lin MJ, Chou YH, Tiu CM, Yeh TJ, Wei JF, Chang T. Zhonghua Yi Xue Za Zhi (Taipei). Although the precise etiology is unknown, an increase in intrathoracic pressure that is transmitted to the jugular vein is believed to cause the venous ectasia. Two children had aneurysmal dilatation of the superficial cervical communicating vein. It is usually a childhood disease and believed to be of congenital origin. Literature reports of bilateral presentation are rare. Internal jugular vein (IJV) ectasia commonly presents as a unilateral, soft, compressible neck swelling, which typically increases in size with straining, valsalva maneuvre, sneezing, bending or coughing. I87.8 is a billable diagnosis code used to specify a medical diagnosis of other specified disorders of veins. Among neck veins, ectasia of the internal jugular vein (IJV) are extremely uncommon. Jugular Vein Ectasia In • Robert W. Jasinski, MD,* Jonathan M. Rubin, MOt Jugular vein aneurysm can mimic more serious abnormalities and produce cosmetic difficulties for patients. Valid for Submission. Three cases of jugular venous ectasia in children were diagnosed preoperatively by selective venography. A typical history and complex of physical findings are associated with this entity. Maximum antero-posterior diameter of left IJV during valsava - 8 mm. Jugular phlebectasia is a congenital dilation of the jugular vein, which is extremely rare in adults, may present similarly. Internal jugular phlebectasia in children. Specific conditions. Duplication of the internal jugular vein (IJV), which is usually encountered coincidentally, is another rare anatomic variation. The possible … The entity was suspected on ultrasound imaging and confirmed by computed tomography scan and Doppler. 15, No. Am J Surg. Jugular Ectasia is a rare benign swelling due to dilatation of jugular vein, which can occur in the internal, external or an anterior jugular vein. It is a benign vascular abnormality but may be un-der-reported possibly due to its benign nature [5]. The existence of marked asymmetry in the sizes of normal jugular veins is known from anatomic studies. Patients with venous ectasia present with intermittent neck swelling and rarely with pain. Usually it presents as an asymptomatic, soft, compressible neck swelling that increases in size on Valsalva's manoeuvre. These rare lesions appear to be congenital dilatations of the veins and should not properly be called aneurysms, as their histological structure is normal. 8, International Journal of Pediatric Otorhinolaryngology, Vol. 57, No. The condition is rare in occurrence and is frequently misdiagnosed and managed inappropriately. 1, © 2021 Radiological Society of North America, Jugular phlebectasia: A manometric study in an unanesthetized patient, Internal jugular phlebectasia in Menkes disease, The sizes of internal jugular veins in Turkish children aged between 7 and 12 years, Jugular phlebectasia: theory of pathogenesis and review of literature, Internal jugular vein phlebectasia: Case report. 71, No. Unable to load your collection due to an error, Unable to load your delegates due to an error. Enter your email address below and we will send you your username, If the address matches an existing account you will receive an email with instructions to retrieve your username. Internal jugular phlebectasia can exist along with duplication of internal jugular vein. 25, No. Swelling pointed by parents - Dilated, non-tortous, non-thrombosed internal jugular vein on right side. 1-3, 19 August 2016 | Vascular Surgery, Vol. It can be primary (congenital) or acquired due to trauma, surgery, infection and tumors. If the address matches an existing account you will receive an email with instructions to reset your password. Reference Indudharan, Quah and Shuaib 2 The vein is abnormally dilated without tortuosity. Extremely rare case of Horner’s syndrome due to jugular venous ectasia demonstrated by computed tomography and intravenous digital subtraction angiography as reported by Inci S et al. 8, Journal of Pediatric Surgery, Vol. It is important to include it in the differential diagnosis of neck masses in children. Case series: Internal jugular vein ectasia in pediatric patients. jugular vein ectasia [Duplex Doppler ultrasound of internal jugular vein ectasia. It is rare to have bilateral neck swelling due to internal jugular vein ectasia… 3, International Journal of Pediatric Otorhinolaryngology, Vol. Case report]. Venous ectasia in the neck is a rare and benign condition. Ectasia of Internal Jugular vein: This was a young adult male with complaint of small swelling in the left side of neck and mild dysphagia. 2, The British Journal of Radiology, Vol. 8, Journal of Pediatric Surgery, Vol. 1 We present two cases in which Jugular vein ectasia is a venous anomaly that commonly presents itself as a unilateral neck swelling in children and adults. 182, No. Bethesda, MD 20894, Copyright Ectasia of the internal jugular vein was once considered rare, but is increasing in apparent frequency due to the wide use of noninvasive diagnostic modalities. Int J Pediatr Otorhinolaryngol. Jugular vein ectasia is a vasodilation (dilatation), which can be diagnosed in both a child and an adult, regardless of gender. However, this is to be kept in mind when considering differentials for laryngocele. Internal jugular vein ectasia is a venous anomaly commonly presenting as a unilateral neck swelling in children and adults. Surgical treatment of jugular vein phlebectasia in children. This site needs JavaScript to work properly. The probable reason for the cough was the pressure exerted by the dilated vein on the vagus nerve. 12, No. Am J Otolaryngol. 1990 Sep;46(3):190-3. High index of suspicion is required to diagnose the condition. Jugular phlebectasia, a dilatation of the jugular veins, is a relatively rare benign condition. Would you like email updates of new search results? IJV ectasia in the neck is a rare entity, especially in adult [4]. 2, No. Jugular vein phlebectasia (JVP) is of unknown etiology and is caused by vein dilatation without to … Careers. Internal jugular vein ectasia (dilatation of the internal jugular vein) is a rare clinical entity, often undiagnosed. 10, Journal of Clinical Neuroscience, Vol. Maximum antero-posterior diameter of right IJV during valsava - 15 mm. Internal jugular vein ectasia is a rare venous anomaly that presents as a fusiform lower neck swelling. Jugular vein ectasia is a venous anomaly that commonly presents itself as a unilateral neck swelling in children and adults. Three cases of jugular venous ectasia in children were diagnosed preoperatively by selective venography. 58, No. Ligation and excision of the dilated vein almost immediately cured her cough. Phlebectasia of jugular veins can cause a similar sign but is rare compared to laryngocele. Privacy, Help Isolated cases or cases associated with IJV ectasia have been reported. Although a benign condition, it can sometimes be associated with hoarseness of voice, horner’s syndrome and hemorrhage. 25, No. 7, International Journal of Pediatric Otorhinolaryngology, Vol. A typical history and complex of physical findings are associated with this entity. 3, The Journal of Laryngology & Otology, Vol. A 57-year-old woman was referred for right neck discomfort that had developed 1 month earlier. 32, No. 24, No. We report five children with a soft mass in the neck due to congenital jugular venous ectasia. It is characterized by painless, soft, compressible unilateral swelling appeared on Valsalva maneuver. Ectasia of external jugular vein is a rare entity presenting as an intermittent neck swelling. Please enable it to take advantage of the complete set of features! 11203. Saccular aneursyms of the internal jugular vein are rare, as opposed to fusiform aneursyms (phlebectasia) found in the pediatric population. It has also been called phlebectasia, venous aneurysm, venous cyst and aneurysmal varix. Sonography of internal jugular venous ectasia in these patients revealed fusiform dilation of the internal jugular vein, and the possibility of thrombus and external compression could be ruled out. It increases in size on straining. 668, Journal of Clinical Ultrasound, Vol. An external jugular venogram revealed the presence of a very large communicating vein at the base of the skull between the internal and external jugular venous drainage systems. Ultrasonography with Doppler before, during and after valsalva manoeuvre is the preferred method for diagnosis. Our report describes right internal jugular vein ectasia in a … Objectives: To recognize the similarities between laryngocele and ectasias of the IJV and the differences in their presentation and management. The condition can be diagnosed by imaging studies in particular during a Valsalva maneuver. 106, No. This report describes a case of an asymptomatic internal jugular vein aneurysm that presented as an enlarging mass in … 2, The British Journal of Radiology, Vol. FOIA 2). A Report of 3 Cases and Review of the Literature, American Journal of Medical Genetics Part A, Vol. Internal jugular vein ectasia is a venous anomaly commonly presenting as a unilateral neck swelling in children and adults. It is believed that such phlebectasia occurs with insufficiency of vein valves, which provokes stagnation of excess blood, or diseases of other organs and systems. 56, No. 108, No. 8600 Rockville Pike Clipboard, Search History, and several other advanced features are temporarily unavailable. 7, Seminars in Roentgenology, Vol. Three had fusiform dilatation of the internal jugular vein, which in one case was associated with dilatation of the ipselateral external jugular vein. It commonly presents as a unilateral, soft, compressible neck swelling that mostly involves the right side. Others terms have also been used in the literature including venous aneurysm, venous cyst, venous ectasia, aneurysmal varix and venectasia [1 2]. Jugular vein aneurysm is a rare morphologic entity. No other abnormality was noted in neck. Prevention and treatment information (HHS). The clinical manifestation, etiology, pathological findings and diagnostic methods of the internal jugular vein ectasia were reviewed with emphasis on the advantages of duplex Doppler ultrasound in confirming the diagnosis. Jugular vein ectasia is a congenital dilatation of the jugular vein presenting as a swelling in the neck. Bilateral Doppler ultrasonography is the diagnostic investigation of choice. Internal jugular vein ectasia is a venous anomaly commonly presenting as a unilateral neck swelling in children and adults. 2, Journal of Oral and Maxillofacial Surgery, Vol. National Library of Medicine Accurate diagnosis from careful history, physical examination and radiological study can be made. 22, No. 12, 18 August 2016 | Vascular Surgery, Vol. On Color Doppler examination of the vessels of the neck, the right side showed normal diameter and flow in the right internal jugular vein … Ectasia (/ ɛ k ˈ t eɪ ʒ ə /), also called ectasis (/ ˈ ɛ k t ə s ɪ s /), is dilation or distention of a tubular structure, either normal or pathophysiologic but usually the latter (except in atelectasis, where absence of ectasis is the problem).. Marked variation in size of ectatic jugular veins during respiration was demonstrated under real-time sonography. Jugular phlebectasia in children: Is it rare or ignored? PMID: 2178051 [Indexed for MEDLINE] Publication Types: Case Reports; MeSH terms. 1999 Nov-Dec;20(6):415-8. doi: 10.1016/s0196-0709(99)90085-6. Typically, a venous ectasia has no clinical significance other than a cosmetic appearance. 8 Rarely, such ectasias can thrombose, cause athrombophlebitis, or even erode the adjacent mandible. 4, The Journal of Laryngology & Otology, Vol. 10, No. These rare lesions appear to be congenital dilatations of the veins and should not properly be called aneurysms, as their histological structure is normal. 6, Surgical Neurology International, Vol. 26, No. The code I87.8 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions. Although a benign condition, it can sometimes be associated with hoarseness of voice, horner’s syndrome and hemorrhage. Enter your email address below and we will send you the reset instructions. Introduction: Venous ectasia is rare causes of neck mass. 34, No. Bronchiectasis, chronic dilatation of the bronchi; Duct ectasia of breast, a dilated milk duct. 61, No. Internal jugular vein malformation with mature adipose deposits in the mediastinum, Venous aneurysms: Surgical indications and review of the literature, Aneurysm of External Jugular Vein: Case Report and Review of Literature—A Case Report, Internal jugular phlebectasia in two siblings: Manometric and histopathologic studies of the pathogenesis, Swollen neck in children: A report of two cases, The superior vena cava: Conventional projections, Aneurysm of the Internal Jugular Vein — A Case Report, Ultrasonic diagnosis of bilateral congenital internal jugular venous aneurysms, Ultrasonic diagnosis of jugular venous aneurysm, Department of Radiology, State University of New York, Downstate Medical Center, Brooklyn, N. Y. It is the dilatation or aneurysm of the venous system of the neck that may arise from the internal jugular, external jugular or superficial veins. Jugular vein ectasia is a congenital dilatation of the jugular vein presenting as a swelling in the neck. 8, International Journal of Pediatric Otorhinolaryngology, Vol. Usually it presents as an asymptomatic, soft, compressible neck swelling that increases in size on Valsalva's manoeuvre. Introduction. In addition there was retrograde filling of a large plexus of veins corresponding to the parotid area (Fig. Jugular phlebectasia, a benign condition, refers to an isolated abnormal fusiform or saccular dilatation of the jugular vein of unknown etiology. Internal jugular vein ectasia (dilatation of the internal jugular vein) is a rare clinical entity, often undiagnosed. 731, 18 August 2016 | Vascular Surgery, Vol. Venous ectasia, also called phlebectasia or venous aneurysm, is an isolated saccular or fusiform dilatation of a vein.